International Statistical Classification of Diseases and Related Health Problems 10th Revision (ICD-10)-WHO Version for ;2019-covid-expanded

Chapter VI
Diseases of the nervous system
(G00-G99)

Systemic atrophies primarily affecting the central nervous system
(G10-G14)

G10 Huntington disease

Incl.:
Huntington chorea

G11 Hereditary ataxia

Excl.:
cerebral palsy (G80.-)
hereditary and idiopathic neuropathy (G60.-)
metabolic disorders (E70-E90)
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
Note:

Onset usually before the age of 20

Incl.:
Early-onset cerebellar ataxia with:
  • essential tremor
  • myoclonus [Hunt ataxia]
  • retained tendon reflexes
Friedreich ataxia (autosomal recessive)
X-linked recessive spinocerebellar ataxia
G11.2 Late-onset cerebellar ataxia
Note:

Onset usually after the age of 20

G11.3 Cerebellar ataxia with defective DNA repair
Incl.:
Ataxia telangiectasia [Louis-Bar]
Excl.:
Cockayne syndrome (Q87.1)
xeroderma pigmentosum (Q82.1)
G11.4 Hereditary spastic paraplegia
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified
Incl.:
Hereditary cerebellar:
  • ataxia NOS
  • degeneration
  • disease
  • syndrome

G12 Spinal muscular atrophy and related syndromes

G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
G12.1 Other inherited spinal muscular atrophy
Incl.:
Progressive bulbar palsy of childhood [Fazio-Londe]
Spinal muscular atrophy:
  • adult form
  • childhood form, type II
  • distal
  • juvenile form, type III [Kugelberg-Welander]
  • scapuloperoneal form
G12.2 Motor neuron disease
Incl.:
Familial motor neuron disease
Kennedy disease
Lateral sclerosis:
  • amyotrophic
  • primary
Progressive:
  • bulbar palsy
  • spinal muscular atrophy
G12.8 Other spinal muscular atrophies and related syndromes
G12.9 Spinal muscular atrophy, unspecified

G13* Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere

G13.0* Paraneoplastic neuromyopathy and neuropathy
Incl.:
Carcinomatous neuromyopathy (C00-C97†)
Sensorial paraneoplastic neuropathy [Denny Brown] (C00-D48†)
G13.1* Other systemic atrophy primarily affecting central nervous system in neoplastic disease
Incl.:
Paraneoplastic limbic encephalopathy (C00-D48†)
G13.2* Systemic atrophy primarily affecting central nervous system in myxoedema (E00.1†, E03.-†)
G13.8* Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere

G14 Postpolio syndrome

Incl.:
Postpolio myelitic syndrome
Excl.:
sequelae of poliomyelitis (B91)